<![CDATA[Scimitar Syndrome]]> https://www.benthamscience.com RSS Feed for Disease Wise Article | BenthamScience EurekaSelect (+http://eurekaselect.com) Sun, 08 Dec 2024 14:39:55 +0000 <![CDATA[Scimitar Syndrome]]> https://www.benthamscience.com https://www.benthamscience.com <![CDATA[Rarer Components of a Rare Disease: Accessory Hemidiaphragm and Horseshoe Lung with Scimitar Syndrome: Two Case Reports]]>https://www.benthamscience.comarticle/130316Introduction: Scimitar syndrome is a rare developmental anomaly with an incidence of 2/100.000 births. Major components of this disease are partial anomalous pulmonary venous drainage, pulmonary hypoplasia, systemic arterialization of the right basal lung, and dextroposition of the heart. Horseshoe lung and accessory hemidiaphragm are two rarer components of this disease.

Case Presentation: In this paper, horseshoe lung and accessory diaphragm associated with Scimitar syndrome have been reported in two cases.

Conclusion: In conclusion, being aware of rare manifestations of rare diseases is important to fully describe the pathologic spectrum of the disease. This will assist in better management and decision-making process.

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<![CDATA[Diagnostic Strategy for Suspected Unilateral Absence of the Pulmonary Artery]]>https://www.benthamscience.comarticle/139261Background: Unilateral absence of the pulmonary artery (UAPA) is a very rare congenital anomaly.

Objective: To analyze the diagnostic strategy applied to seven patients with UAPA who were examined and subsequently treated at the National Lung Hospital, Hanoi, Vietnam.

Methods: All seven patients, including three pediatric cases (1, 2, and 14 years old) and four adult cases (21, 26, 44, and 53 years old), had a history of recurrent pneumonia, and the clinical symptoms on admission included cough, progressive dyspnea, chest pain, and fatigue. The patients were initially examined clinically, followed by hematological testing, blood biochemistry testing, and chest X-ray radiology. The results suggested UAPA, so echocardiography and contrast-enhanced chest computed tomography (CT) were performed as soon as practical.

Results: The echocardiographic and CT imaging findings confirmed the suspected diagnosis of UAPA in all seven patients, which was accompanied by congenital heart disease in three patients. Three of the seven patients had mild and medium pulmonary hypertension. All seven patients were treated with drugs, which led to improvement in symptoms.

Conclusion: Frontal chest X-ray provided the initial signs suggesting a diagnosis of UAPA. Subsequent echocardiography and contrast-enhanced chest CT were effective diagnostic tools for fast and accurate confirmation of UAPA.

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<![CDATA[Group 5 Pulmonary Hypertension: Multiple Systemic Diseases, Multiple Mechanisms of Pulmonary Hypertension, and Multiple Management Challenges]]>https://www.benthamscience.comarticle/138833 <![CDATA[Variations and Abnormalities of Major Thoracic Vascular Structures]]>https://www.benthamscience.comarticle/61404

Materials and Methods: In this retrospective study, 2,479 patients who underwent thoracic computed tomography between May 2006 and October 2007 in the Radiation Department at Dicle University’s School of Medicine were examined. Of these patients, 1,389 were male and 1,090 were female. No variations or abnormalities were detected in 1,588 of the patients.

Results: In 1,588 out of 2,479 patients (64.1%), no abnormalities or variations were detected. The most frequently detected variations occurred in the brachiocephalic trunk and the sole root point of the carotid artery from the aorta; these variations were detected in 838 (33.8%) patients.

In 74 of the 2,479 patients (3.0%) examined, it was found that the left vertebral artery directly initiated from the arch of the aorta. In addition, in 33 patients, the right brachiocephalic trunk and left major carotid artery initiated from the aorta as a single root.

Conclusion: Via multi-slice CT, it is possible to detect variations and abnormalities of major thoracic vascular structures; therefore, there is no need for extra diagnostic invasive digital subtraction angiography.]]> <![CDATA[Raman Spectroscopy and Imaging: Promising Optical Diagnostic Tools in Pediatrics]]>https://www.benthamscience.comarticle/50792 <![CDATA[ A Sensitive Voltammetric Sensor for Detecting Betamethasone in Biological Fluids]]>https://www.benthamscience.comarticle/16902